Distal weakness pattern involving face, hands, and forearms is characteristic of which dystrophy?

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Multiple Choice

Distal weakness pattern involving face, hands, and forearms is characteristic of which dystrophy?

Explanation:
Distal weakness with facial involvement is a hallmark of myotonic dystrophy. This condition features myotonia (delayed relaxation after contraction) and weakness that often starts in distal muscles of the hands and forearms, while also affecting facial muscles, producing ptosis and facial weakness. By contrast, Duchenne/Becker and limb-girdle muscular dystrophies mostly affect proximal muscles—the shoulder/hip girdles—early on, with less emphasis on the face and distal hand/forearm muscles. So the described pattern best fits myotonic dystrophy.

Distal weakness with facial involvement is a hallmark of myotonic dystrophy. This condition features myotonia (delayed relaxation after contraction) and weakness that often starts in distal muscles of the hands and forearms, while also affecting facial muscles, producing ptosis and facial weakness. By contrast, Duchenne/Becker and limb-girdle muscular dystrophies mostly affect proximal muscles—the shoulder/hip girdles—early on, with less emphasis on the face and distal hand/forearm muscles. So the described pattern best fits myotonic dystrophy.

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